Craniosynostosis

Craniosynostosis

Normal fusion of the coronal, lambdoidal, squamosal and sagittal sutures occurs between 6 and 12 months of age; others such as the frontal suture fuse later. Craniosynostosis is the premature fusion of one (simple craniosynostosis) or more (complex craniosynostosis) cranial sutures, preventing growth - perpendicular to the suture. This results in a range of skull deformities ( Table 48.8 and Figures 48.29 and 48.30 ) and hydrocephalus. Syndromic craniosynostosis, often associated - with abnormalities of the fibroblast growth factor receptor genes, is accompanied by developmental delay and other abnormalities. The surgical treatment aims to correct defor - mity and prevent development of raised ICP . -

TABLE 48.8 Types of craniosynostosis. Type Suture involved Clinical features Scaphocephaly Sagittal suture Narrow boat-shaped head Brachycephaly Coronal suture Shortened/broad forehead Microcephaly All sutures involved Small head Plagiocephaly Unilateral coronal/ Asymmetric skull lambdoid suture Trigonocephaly Metopic suture Pointed narrow forehead

Craniosynostosis

Normal fusion of the coronal, lambdoidal, squamosal and sagittal sutures occurs between 6 and 12 months of age; others such as the frontal suture fuse later. Craniosynostosis is the premature fusion of one (simple craniosynostosis) or more (complex craniosynostosis) cranial sutures, preventing growth - perpendicular to the suture. This results in a range of skull deformities ( Table 48.8 and Figures 48.29 and 48.30 ) and hydrocephalus. Syndromic craniosynostosis, often associated - with abnormalities of the fibroblast growth factor receptor genes, is accompanied by developmental delay and other abnormalities. The surgical treatment aims to correct defor - mity and prevent development of raised ICP . -

TABLE 48.8 Types of craniosynostosis. Type Suture involved Clinical features Scaphocephaly Sagittal suture Narrow boat-shaped head Brachycephaly Coronal suture Shortened/broad forehead Microcephaly All sutures involved Small head Plagiocephaly Unilateral coronal/ Asymmetric skull lambdoid suture Trigonocephaly Metopic suture Pointed narrow forehead

Craniosynostosis

Normal fusion of the coronal, lambdoidal, squamosal and sagittal sutures occurs between 6 and 12 months of age; others such as the frontal suture fuse later. Craniosynostosis is the premature fusion of one (simple craniosynostosis) or more (complex craniosynostosis) cranial sutures, preventing growth - perpendicular to the suture. This results in a range of skull deformities ( Table 48.8 and Figures 48.29 and 48.30 ) and hydrocephalus. Syndromic craniosynostosis, often associated - with abnormalities of the fibroblast growth factor receptor genes, is accompanied by developmental delay and other abnormalities. The surgical treatment aims to correct defor - mity and prevent development of raised ICP . -

TABLE 48.8 Types of craniosynostosis. Type Suture involved Clinical features Scaphocephaly Sagittal suture Narrow boat-shaped head Brachycephaly Coronal suture Shortened/broad forehead Microcephaly All sutures involved Small head Plagiocephaly Unilateral coronal/ Asymmetric skull lambdoid suture Trigonocephaly Metopic suture Pointed narrow forehead