Prognosis

Prognosis

Prognosis is poor – sometimes considered the ‘motor neurone disease’ of the gut. Infantile forms have a mortality of approx imately 50%. This is generally lower in adult forms depending on cause and avoiding repeated surgery and overuse of opioid Harald Hirschsprung , 1830–1916, physician, The Queen Louise Hospital for Children, Copenhagen, Denmark, described congenital megacolon in 1887. ity and progression to type II/III intestinal failure with the need f or lifelong parenteral nutrition.