Radial club hand

Radial club hand

This longitudinal failure of formation is commonly associ - ated with other malformations, for example as part of the V ACTERL (abnormal vertebrae, anus, cardiovascular system, trachea, oesophagus, renal system and limb buds) syndr ome. The clinical problem depends on whether the thumb is present and functional ( Figure 44.32 ). Treatment is a balance of conservative measures, including physiotherapy and splinting, and judicious surgery to centralise and stabilise the hand and wrist on the single bone forearm. Thumb reconstruction may ) but be technically challenging. In later childhood, forearm length - ening may be considered.

affecting the hand. Anomaly De /f_i nition Treatment Extra/accessory Excise/amputate when digits necessary Failure of separation Syndactyly Separation with/ of digits without skin grafting for functional or cosmetic reasons Trigger thumb Release of the A1 (digit) pulley of the /f_l exor tendon sheath Surgical treatment of Abnormal angulation Clinodactyly the delta phalanx if of the digit in the (usually the /f_i fth deformity is progressive radioulnar plane digit) or interfering with hand function Splinting/ Fixed /f_l exion Camptodactyly physiotherapy; surgery deformity of (usually the /f_i fth rarely indicated the proximal digit) interphalangeal joint Figure 44.32 Anteroposterior radiograph of a radial club hand demon strating a short radius, a deformed ulna and an absent thumb.

Radial club hand

This longitudinal failure of formation is commonly associ - ated with other malformations, for example as part of the V ACTERL (abnormal vertebrae, anus, cardiovascular system, trachea, oesophagus, renal system and limb buds) syndr ome. The clinical problem depends on whether the thumb is present and functional ( Figure 44.32 ). Treatment is a balance of conservative measures, including physiotherapy and splinting, and judicious surgery to centralise and stabilise the hand and wrist on the single bone forearm. Thumb reconstruction may ) but be technically challenging. In later childhood, forearm length - ening may be considered.

affecting the hand. Anomaly De /f_i nition Treatment Extra/accessory Excise/amputate when digits necessary Failure of separation Syndactyly Separation with/ of digits without skin grafting for functional or cosmetic reasons Trigger thumb Release of the A1 (digit) pulley of the /f_l exor tendon sheath Surgical treatment of Abnormal angulation Clinodactyly the delta phalanx if of the digit in the (usually the /f_i fth deformity is progressive radioulnar plane digit) or interfering with hand function Splinting/ Fixed /f_l exion Camptodactyly physiotherapy; surgery deformity of (usually the /f_i fth rarely indicated the proximal digit) interphalangeal joint Figure 44.32 Anteroposterior radiograph of a radial club hand demon strating a short radius, a deformed ulna and an absent thumb.

Radial club hand

This longitudinal failure of formation is commonly associ - ated with other malformations, for example as part of the V ACTERL (abnormal vertebrae, anus, cardiovascular system, trachea, oesophagus, renal system and limb buds) syndr ome. The clinical problem depends on whether the thumb is present and functional ( Figure 44.32 ). Treatment is a balance of conservative measures, including physiotherapy and splinting, and judicious surgery to centralise and stabilise the hand and wrist on the single bone forearm. Thumb reconstruction may ) but be technically challenging. In later childhood, forearm length - ening may be considered.

affecting the hand. Anomaly De /f_i nition Treatment Extra/accessory Excise/amputate when digits necessary Failure of separation Syndactyly Separation with/ of digits without skin grafting for functional or cosmetic reasons Trigger thumb Release of the A1 (digit) pulley of the /f_l exor tendon sheath Surgical treatment of Abnormal angulation Clinodactyly the delta phalanx if of the digit in the (usually the /f_i fth deformity is progressive radioulnar plane digit) or interfering with hand function Splinting/ Fixed /f_l exion Camptodactyly physiotherapy; surgery deformity of (usually the /f_i fth rarely indicated the proximal digit) interphalangeal joint Figure 44.32 Anteroposterior radiograph of a radial club hand demon strating a short radius, a deformed ulna and an absent thumb.